{"id":462,"date":"2024-03-21T06:54:05","date_gmt":"2024-03-21T05:54:05","guid":{"rendered":"https:\/\/associationkabanon.fr\/?page_id=462"},"modified":"2024-03-21T06:54:05","modified_gmt":"2024-03-21T05:54:05","slug":"le-syndrome-kabuki","status":"publish","type":"page","link":"https:\/\/associationkabanon.fr\/index.php\/le-syndrome-kabuki\/","title":{"rendered":"Le syndr\u00f4me Kabuki"},"content":{"rendered":"\n<p><a href=\"https:\/\/www.orpha.net\/pdfs\/data\/patho\/Han\/Int\/fr\/SyndromeKabuki_FR_fr_HAN_ORPHA2322.pdf\">https:\/\/www.orpha.net\/pdfs\/data\/patho\/Han\/Int\/fr\/SyndromeKabuki_FR_fr_HAN_ORPHA2322.pdf<\/a><\/p>\n\n\n\n<p>Le <strong>syndrome de Niikawa-Kuroki<\/strong>, plus commun\u00e9ment surnomm\u00e9 <strong>syndrome kabuki<\/strong> est une maladie <a href=\"https:\/\/fr.wikipedia.org\/wiki\/Maladie_g%C3%A9n%C3%A9tique\"><u>cong\u00e9nitale<\/u><\/a> associant&nbsp;:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>un <a href=\"https:\/\/fr.wikipedia.org\/wiki\/Retard_psychomoteur\"><u>retard psychomoteur<\/u><\/a>&nbsp;;<\/li>\n\n\n\n<li>un visage caract\u00e9ristique pr\u00e9sentant quelques similarit\u00e9s avec le maquillage des acteurs du th\u00e9\u00e2tre japonais <a href=\"https:\/\/fr.wikipedia.org\/wiki\/Kabuki\"><u>kabuki<\/u><\/a>&nbsp;;<\/li>\n\n\n\n<li>un retard de croissance d&#8217;apparition le plus souvent apr\u00e8s la naissance&nbsp;;<\/li>\n\n\n\n<li>des particularit\u00e9s des plis des mains (dermatoglyphes) et la persistance de l&#8217;aspect f\u0153tal des pulpes des doigts (aspects en gouttes d&#8217;eau)&nbsp;;<\/li>\n\n\n\n<li>et des anomalies du squelette, dont une <a href=\"https:\/\/fr.wikipedia.org\/wiki\/Scoliose\"><u>scoliose<\/u><\/a> et un raccourcissement du cinqui\u00e8me <a href=\"https:\/\/fr.wikipedia.org\/wiki\/Doigt\"><u>doigt<\/u><\/a>.<\/li>\n<\/ul>\n\n\n\n<p>Le nom de ce <a href=\"https:\/\/fr.wikipedia.org\/wiki\/Syndrome\"><u>syndrome<\/u><\/a> est en rapport avec les acteurs du <a href=\"https:\/\/fr.wikipedia.org\/wiki\/Kabuki\"><u>kabuki<\/u><\/a>, th\u00e9\u00e2tre traditionnel japonais.<\/p>\n","protected":false},"excerpt":{"rendered":"<p>https:\/\/www.orpha.net\/pdfs\/data\/patho\/Han\/Int\/fr\/SyndromeKabuki_FR_fr_HAN_ORPHA2322.pdf Le syndrome de Niikawa-Kuroki, plus commun\u00e9ment surnomm\u00e9 syndrome kabuki est une maladie cong\u00e9nitale associant&nbsp;: Le nom de ce syndrome est en rapport avec les acteurs du kabuki, th\u00e9\u00e2tre traditionnel japonais.<\/p>\n","protected":false},"author":2,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"neve_meta_sidebar":"","neve_meta_container":"","neve_meta_enable_content_width":"","neve_meta_content_width":0,"neve_meta_title_alignment":"","neve_meta_author_avatar":"","neve_post_elements_order":"","neve_meta_disable_header":"","neve_meta_disable_footer":"","neve_meta_disable_title":"","_themeisle_gutenberg_block_has_review":false,"footnotes":""},"class_list":["post-462","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/pages\/462","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/comments?post=462"}],"version-history":[{"count":1,"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/pages\/462\/revisions"}],"predecessor-version":[{"id":463,"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/pages\/462\/revisions\/463"}],"wp:attachment":[{"href":"https:\/\/associationkabanon.fr\/index.php\/wp-json\/wp\/v2\/media?parent=462"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}